J86

RENAL DYSPLASIA (right) & AGENESIS (left)

Description
The left kidney is absent. The right kidney is a multicytstic mass with a blood supply from the aorta and without a ureter. The adrenal glands are discoid rather than globular in outline as one would expect with displacement of one kidney and the absence of the second.
History
The baby was delivered prematurely as a breech at an estimated gestational age of 33 weeks. Oliohydramnios was noted. The child survived approximately 30 hours, was aneuric and in respiratory failure. At autopsy there was evidence in addition to the present findings, of pulmonary hypoplasia.